Anesthetic Management in Pediatric Patient with Prader-Willi Syndrome: A case report.

Min,  Sam Hong; Lim,  Choon Hak; Lee,  Hye Won; Lim,  Hae Ja; Yoon,  Suk Min; Chang,  Seong Ho

doi:2004.47.3.439

Korean J Anesthesiol > Volume 47(3); 2004 > Article

Case Report

Korean Journal of Anesthesiology 2004;47(3):439-441.
DOI: https://doi.org/10.4097/kjae.2004.47.3.439

Anesthetic Management in Pediatric Patient with Prader-Willi Syndrome: A case report.

Sam Hong Min, Choon Hak Lim, Hye Won Lee, Hae Ja Lim, Suk Min Yoon, Seong Ho Chang

Department of Anesthesiology and Pain Medicine, College of Medicine, Korea University, Seoul, Korea. torchid@korea.ac.kr

Abstract

Prader-Willi syndrome is brought by chromosomal abnormality and is characterized by mental retardation, morbid obesity, infantile hypotonia, hypogenitalism. While feeding problems arise during infancy due to hypotonia, it is followed by hyperphasia that is prone to morbid obesity leading to cardiovascular problems, diabetes, and infectious diseases. And sleep apnea, scoliosis make anesthetic management difficult. We report a case of general anesthetic management during strabismus surgery in a child with Prader-Willi syndrome and its possible considerations.

Key Words: anesthetic management; Prader Willi syndrome