| Anesthetic experience of a pediatric patient with Seckel syndrome associated with pneumonia : A case report. |
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Tae Hee Kim, Young Uk Kim, Jun Gol Song, Jai Hyun Hwang |
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Department of Anesthesiology and Pain Medicine, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Korea. jaljary@naver.com |
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| Abstract |
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Seckel syndrome, also called bird-headed dwarfism, is an extremely rare, inherited, autosomal recessive disorder. The patients with Seckel syndrome are characterized by growth retardation, microcephaly with mental retardation, proportional dwarfism, bird like faces, and beak-like triangular nose. A literature review reveals that they have multiple anesthetic problems such as difficult airway management, difficult venous cannulation and concomitant medical diseases. We describe our experience in anesthetic management of a 21-month-old male patient with Seckel syndrome associated with pneumonia who underwent orchiopexy for bilateral cryptochidism. |
| Key Words:
Airway management; Bird-headed dwarfism; Seckel syndrome |
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