Tracheal Agenesis: A case report. |
Ji Yung Lee, Sang Youp Kim, Kyo Young Lee, Se Ho Moon |
1Department of Anesthesiology, Catholic University Medical College, Seoul, Korea. 2Department of Clinical Pathology, Catholic University Medical College, Seoul, Korea. |
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Abstract |
Agenesis of trachea is a rare congenital anomaly. The main signs are respiratory distress, cyanosis, inability to vocalise and impossible tracheal intubation. There is no long-term surgical solution at present, therefore the condition is ultimately fatal. We report a case of tracheal agenesis. We anesthetized a 2.25 kg neonate for endoscopic examination, who was intubated successfully. Beyond 2.5 cm from the vocal cord, there was no trachea and we can only see esophageal lumen with fistula opening. After the endoscopic examination, exploratory thoracotomy was done, but surgical correction was impossible. After the surgery, she died from progressive ventilatory failure. Autopsy revealed a Floyd's type II tracheal agenesis with tracheo-esophageal fistula. |
Key Words:
Lung: respiratory distress syndrome; tracheal agenesis; tracheoesophageal fistula |
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