Anesthetic Management of a Patient with Tuberous Sclerosis Undergoing Bilateral Nephrectomy: A case report. |
Dongchul Lee, Kyung Cheon Lee, Hong Sun Kim, Hyun Jeong Kwak, Ki Tae Moon |
Department of Anesthesiology and Pain Medicine, Gacheon Medical School Gil Medical Center, Incheon, Korea. hyun615@hanmail.net |
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Abstract |
Tuberous sclerosis is an autosomal dominantly transmitted genetic disorder that has characteristic symptoms triad of mental retardation, convulsion, and facial angiofibroma.
Because it is a relatively uncommon disorder, there are few informations about anesthetic management for this disorder.
We report a case of tuberous sclerosis that had involved bilateral kidneys. A 14-year old female patient was induced with thiopental sodium, rocuronium bromide and then intubated with an internal diameter 6.5 mm of reinforced tube. Anesthesia was maintained with O2-N2O-isoflurane.
Surgery took 3 hours and there were no remarkable changes in vital signs and arterial blood gas analysis. |
Key Words:
anesthesia; nephrectomy; tuberous sclerosis |
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